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KMID : 0985520130180030028
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Korean Journal of Pancreas and Biliary Tract
2013 Volume.18 No. 3 p.28 ~ p.31
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A Case of Idiopathic Adulthood Ductopenia
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Kang Jin-Gu
Jang Myoung-Kuk
Lee Ji-Un
Kim Eun-Jung
Kim Mi-Hee
Yang Bo-Kyung
Cho Seong-Jin
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Abstract
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Idiopathic adulthood ductopenia (IAD) is a rare adult onset chronic cholestatic disease of unknown etiology without the existence of inflammatory bowel disease. IAD has characteristics of autoantibody absence in lab findings and loss of interlobular bile ducts in biopsy. A 28-year-old man admitted to the hospital with an incidental finding of elevated transaminases and alkaline phosphatase on routine health screening. The viral hepatitis markers and autoimmune hepatitis antibodies were all negative. The patient showed a radiologically normal anatomy of extrahepatic biliary tree. Histological examination of four liver biopsy specimens showed severe ductopenia on all portal tracts. We, herein, report a rare case of IAD with a brief review of literature.
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KEYWORD
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idiopathic adulthood ductopenia, cholestasis
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